Reaction Details |
| Report a problem with these data |
Target | Lysosomal alpha-glucosidase |
---|
Ligand | BDBM190536 |
---|
Substrate/Competitor | n/a |
---|
Meas. Tech. | Enzyme Activity Assay |
---|
pH | 4±n/a |
---|
EC50 | 121000±11400 nM |
---|
Comments | extracted |
---|
Citation | Mugrage, B; Lee, G; Zhu, X; Boyd, R; Sheth, K Method for the treatment of pompe disease using 1-deoxynojirimycin and derivatives US Patent US9181184 Publication Date 11/10/2015 |
---|
More Info.: | Get all data from this article, Assay Method |
---|
|
Lysosomal alpha-glucosidase |
---|
Name: | Lysosomal alpha-glucosidase |
Synonyms: | α-Glucosidase | Acid maltase | Gaa | LYAG_MOUSE | Lysosomal alpha-glucosidase | alpha-glucosidase (Gaa) |
Type: | Enzyme |
Mol. Mass.: | 106235.32 |
Organism: | Mus musculus (Mouse) |
Description: | P70699 |
Residue: | 953 |
Sequence: | MNIRKPLCSNSVVGACTLISLTTAVILGHLMLRELMLLPQDLHESSSGLWKTYRPHHQEG
YKPGPLHIQEQTEQPKEAPTQCDVPPSSRFDCAPDKGISQEQCEARGCCYVPAGQVLKEP
QIGQPWCFFPPSYPSYRLENLSSTESGYTATLTRTSPTFFPKDVLTLQLEVLMETDSRLH
FKIKDPASKRYEVPLETPRVLSQAPSPLYSVEFSEEPFGVIVRRKLGGRVLLNTTVAPLF
FADQFLQLSTSLPSQHITGLGEHLSPLMLSTDWARITLWNRDTPPSQGTNLYGSHPFYLA
LEDGGLAHGVFLLNSNAMDVILQPSPALTWRSTGGILDVYVFLGPEPKSVVQQYLDVVGY
PFMPPYWGLGFHLCRWGYSSTAIVRQVVENMTRTHFPLDVQWNDLDYMDARRDFTFNQDS
FADFPDMVRELHQDGRRYMMIVDPAISSAGPAGSYRPYDEGLRRGVFITNETGQPLIGKV
WPGTTAFPDFTNPETLDWWQDMVSEFHAQVPFDGMWLDMNEPSNFVRGSQQGCPNNELEN
PPYVPGVVGGILQAATICASSHQFLSTHYNLHNLYGLTEAIASSRALVKTRGTRPFVISR
STFSGHGRYAGHWTGDVRSSWEHLAYSVPDILQFNLLGVPLVGADICGFIGDTSEELCVR
WTQLGAFYPFMRNHNDLNSVPQEPYRFSETAQQAMRKAFALRYALLPYLYTLFHRAHVRG
DTVARPLFLEFPEDPSTWSVDRQLLWGPALLITPVLEPGKTEVTGYFPKGTWYNMQMVSV
DSLGTLPSPSSASSFRSAVQSKGQWLTLEAPLDTINVHLREGYIIPLQGPSLTTTESRKQ
PMALAVALTASGEADGELFWDDGESLAVLERGAYTLVTFSAKNNTIVNKLVRVTKEGAEL
QLREVTVLGVATAPTQVLSNGIPVSNFTYSPDNKSLAIPVSLLMGELFQISWS
|
|
|
BDBM190536 |
---|
n/a |
---|
Name | BDBM190536 |
Synonyms: | US9181184, 23 |
Type | Small organic molecule |
Emp. Form. | C14H18F3NO4 |
Mol. Mass. | 321.2922 |
SMILES | OC[C@@H]1[C@@H](O)[C@H](O)[C@@H](O)CN1Cc1ccc(cc1)C(F)(F)F |r| |
Structure |
|