Reaction Details |
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Target | Lysosomal alpha-glucosidase |
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Ligand | BDBM18364 |
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Substrate/Competitor | n/a |
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Meas. Tech. | Enzyme Activity Assay |
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pH | 4±n/a |
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EC50 | 7000±1800 nM |
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Comments | extracted |
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Citation | Mugrage, B; Lee, G; Zhu, X; Boyd, R; Sheth, K Method for the treatment of pompe disease using 1-deoxynojirimycin and derivatives US Patent US9181184 Publication Date 11/10/2015 |
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More Info.: | Get all data from this article, Assay Method |
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Lysosomal alpha-glucosidase |
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Name: | Lysosomal alpha-glucosidase |
Synonyms: | α-Glucosidase | Acid maltase | Gaa | LYAG_MOUSE | Lysosomal alpha-glucosidase | alpha-glucosidase (Gaa) |
Type: | Enzyme |
Mol. Mass.: | 106235.32 |
Organism: | Mus musculus (Mouse) |
Description: | P70699 |
Residue: | 953 |
Sequence: | MNIRKPLCSNSVVGACTLISLTTAVILGHLMLRELMLLPQDLHESSSGLWKTYRPHHQEG
YKPGPLHIQEQTEQPKEAPTQCDVPPSSRFDCAPDKGISQEQCEARGCCYVPAGQVLKEP
QIGQPWCFFPPSYPSYRLENLSSTESGYTATLTRTSPTFFPKDVLTLQLEVLMETDSRLH
FKIKDPASKRYEVPLETPRVLSQAPSPLYSVEFSEEPFGVIVRRKLGGRVLLNTTVAPLF
FADQFLQLSTSLPSQHITGLGEHLSPLMLSTDWARITLWNRDTPPSQGTNLYGSHPFYLA
LEDGGLAHGVFLLNSNAMDVILQPSPALTWRSTGGILDVYVFLGPEPKSVVQQYLDVVGY
PFMPPYWGLGFHLCRWGYSSTAIVRQVVENMTRTHFPLDVQWNDLDYMDARRDFTFNQDS
FADFPDMVRELHQDGRRYMMIVDPAISSAGPAGSYRPYDEGLRRGVFITNETGQPLIGKV
WPGTTAFPDFTNPETLDWWQDMVSEFHAQVPFDGMWLDMNEPSNFVRGSQQGCPNNELEN
PPYVPGVVGGILQAATICASSHQFLSTHYNLHNLYGLTEAIASSRALVKTRGTRPFVISR
STFSGHGRYAGHWTGDVRSSWEHLAYSVPDILQFNLLGVPLVGADICGFIGDTSEELCVR
WTQLGAFYPFMRNHNDLNSVPQEPYRFSETAQQAMRKAFALRYALLPYLYTLFHRAHVRG
DTVARPLFLEFPEDPSTWSVDRQLLWGPALLITPVLEPGKTEVTGYFPKGTWYNMQMVSV
DSLGTLPSPSSASSFRSAVQSKGQWLTLEAPLDTINVHLREGYIIPLQGPSLTTTESRKQ
PMALAVALTASGEADGELFWDDGESLAVLERGAYTLVTFSAKNNTIVNKLVRVTKEGAEL
QLREVTVLGVATAPTQVLSNGIPVSNFTYSPDNKSLAIPVSLLMGELFQISWS
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BDBM18364 |
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n/a |
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Name | BDBM18364 |
Synonyms: | (2R,3R,4R,5S,6R)-2-(hydroxymethyl)-6-nonylpiperidine-3,4,5-triol | CN-DNJ | US9181184, 32 | alpha-1-C-Nonyl-DNJ |
Type | Small organic molecule |
Emp. Form. | C15H31NO4 |
Mol. Mass. | 289.4109 |
SMILES | CCCCCCCCC[C@H]1N[C@H](CO)[C@@H](O)[C@H](O)[C@H]1O |
Structure |
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